Ectodermal dysplasia is a specific syndrome characterized by a congenital dysplasia of one or more ectodermal structures and their accessory appendages, manifested primarily by hypohydrosis and hypodontia. Patient with this abnormality invariably
manifest anodontia of oligodontia with frequent malformation of any teeth present, Since the alveolar process does not develop in the absence of teeth, there is a reduction from normal vertical dimension resulting in the protuberant lips.
In themajority of this diseases, it is an X-linked recessive mendelian character, males being affected much more frequently than females. This paper show male twin ectodermal does not manifest this syndrome. Their parents apprehend that their
sons
sould
be laughed at by friends.
There is no treatment for the condition, although, from dental standpoint, partial or full dentures should be constructed for both functional and cosmetic purpose. First of all, psychological stisfaction of patient is most important.
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